RESUMO
Hemorrhagic lymphatic malformation (formerly called hemolymphangioma) of the tongue is an uncommon malformation that may pose both functional and cosmetic problems for the patient. The challenge has been to find a conservative treatment with low morbidity and better results than those achieved with surgical excision, which has been the mainstay of therapy. We report a case of successful treatment of a hemorrhagic lymphatic malformation of the tongue with a variable-pulse 595-nm pulsed-dye laser (Vbeam; Candela Corp, Wayland, Mass). In this patient, pulsed-dye laser treatment of the hemorrhagic lymphatic malformation achieved satisfactory functional and cosmetic outcomes. Its use in superficial vascular lesions of the mucosa should be considered.
Assuntos
Hemangioma/radioterapia , Terapia a Laser , Linfangioma/radioterapia , Neoplasias da Língua/radioterapia , Adolescente , Feminino , Hemangioma/complicações , Hemorragia/etiologia , Hemorragia/radioterapia , Humanos , Linfangioma/complicações , Neoplasias da Língua/complicaçõesAssuntos
Acrodermatite/patologia , Alopecia/etiologia , Diarreia/etiologia , Zinco/deficiência , Acrodermatite/etiologia , Adulto , Feminino , HumanosAssuntos
Aspergilose/diagnóstico , Aspergillus flavus/isolamento & purificação , Dermatoses Faciais/diagnóstico , Fungemia/diagnóstico , Hospedeiro Imunocomprometido , Leucemia Mieloide Aguda/complicações , Idoso , Aspergilose/complicações , Diagnóstico Diferencial , Dermatoses Faciais/complicações , Evolução Fatal , Fungemia/complicações , Humanos , MasculinoAssuntos
Adjuvantes Imunológicos/uso terapêutico , Aminoquinolinas/uso terapêutico , Recidiva Local de Neoplasia/tratamento farmacológico , Doença de Paget Extramamária/tratamento farmacológico , Neoplasias Vulvares/tratamento farmacológico , Idoso , Aminoquinolinas/administração & dosagem , Feminino , Humanos , ImiquimodeAssuntos
Anticorpos Monoclonais/efeitos adversos , Fármacos Dermatológicos/efeitos adversos , Toxidermias/etiologia , Púrpura/induzido quimicamente , Adulto , Anticorpos Monoclonais/uso terapêutico , Doença de Crohn/tratamento farmacológico , Toxidermias/patologia , Feminino , Humanos , Infliximab , Púrpura/patologiaRESUMO
We present a 32-year-old white patient with congenital reticular ichthyosiform erythroderma, also known as ichthyosis variegata. The patient had typical clinical features with areas of normal appearing skin surrounded by erythematous hyperkeratotic patches. The smaller "confetti-like" patches were mostly present on the trunk, while the larger areas forming a reticular pattern predominated on the extremities. Ultrastructural findings demonstrated perinuclear vacuolization, binuclear cells and filamentous deposits compatible with congenital reticular ichthyosiform erythroderma. Besides presenting the case, we review the literature on this rare disorder of keratinization.